Citation Information :
Nayak RJ, Kumar AS. Dental Management of Prader-Willi Syndrome in a 7-year-old Girl: A Rare Case Report. J South Asian Assoc Pediatr Dent 2022; 5 (2):96-100.
Prader-Willi syndrome (PWS) is a rare genetic disorder characterized by a lack of expression of paternal genes located on chromosome 15q11-q13. Prader-Willi syndrome is characterized by hypothalamic dysfunction. This anomaly causes cognitive, neurological, and endocrine abnormalities, among which hyperphagia is the important feature. Prader-Willi syndrome is of interest to the dentist because PWS is associated with atrophy of salivary glands leading to decreased salivary secretion and increased risk for dental caries and gingivitis. The present case report describes a clinical case of a 7-year-old girl with PWS. The case presented with multiple carious teeth, partial ankyloglossia, and pyogenic granuloma of gingiva. Restorations were done for carious teeth and 64, 83 were extracted under local anesthesia, and an excisional biopsy of the gingival lesion was done. Periodic dental visits and early interventions are needed to improve the oral health of children with PWS.
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