Introduction: Lymphomas are malignant neoplasms arising from lymphocytes B cell or T cell that affects mainly lymph nodes, spleen, and other nonhematopoietic tissues. They are classified as Hodgkin's lymphoma (HL) and non-Hodgkin's lymphoma (NHL). NHL is diagnosed in extranodal sites in 40% of cases, mainly in the head and the neck region, while HL is found in extranodal sites (1-4%) with a lower incidence. Though it is poorly differentiated, rare, and aggressive, but it is known to have the shortest doubling time creating special challenges for diagnosis and treatment. In the oral soft tissues, lesions can occur as hard and diffuse tumors involving oral vestibule, gums, and posterior region of the hard palate. The extent of disease at presentation is the most important prognostic factor in Burkitt's lymphoma. Management: Management modality includes chemotherapy as the mainstay of treatment for this disease; consultation with a hematologist and an oncologist should be obtained as soon as possible. Aim: The following case report depicts a rare case of a 9-year-old male child with an aggressive form of Burkitt-like (BL) lymphoma highlighting the diagnosis, dental management, precautions, and general and dental considerations to be kept in mind in such special patients with immunocompromised status and considerations in such immunocompromised patients.